Spinal paraganglioma as unusual finding in von Hippel-Lindau disease

Publikation

Spinal paraganglioma as unusual finding in von Hippel-Lindau disease

Wissenschaftlicher Artikel/Review - 07.05.2020

Klingler Jan-Helge, Elsheikh Samer, Doostkam Soroush, Krüger Marie, Blass Bianca-Ioana, Steiert Christine

PubMed

32389544

DOI

10.1016/j.jocn.2020.05.025

Zitation

Klingler J, Elsheikh S, Doostkam S, Krüger M, Blass B, Steiert C. Spinal paraganglioma as unusual finding in von Hippel-Lindau disease. J Clin Neurosci 2020; 77:217-221.

Art

Wissenschaftlicher Artikel/Review (Englisch)

Zeitschrift

J Clin Neurosci 2020; 77

Veröffentlichungsdatum

07.05.2020

eISSN (Online)

1532-2653

Seiten

217-221

Kurzbeschreibung/Zielsetzung

A 20-year-old patient with a history of von Hippel-Lindau disease reported on thoracic back pain radiating to the left shoulder for 10 weeks. Magnetic resonance imaging revealed a progressive contrast-enhancing tumor (14 × 21 × 28 mm) compressing the spinal cord and extending into the left neural foramen at T5/6. After embolization of supplying vessels, the tumor was completely resected via hemilaminectomy of T5. The postoperative course was uneventful without surgery related morbidity. The pathological examination disclosed a paraganglioma WHO grade I. We discuss the differential diagnoses and pitfalls of this unexpected finding in this patient with von Hippel-Lindau disease.