Spinal paraganglioma as unusual finding in von Hippel-Lindau disease

Publication

Spinal paraganglioma as unusual finding in von Hippel-Lindau disease

Journal Paper/Review - May 7, 2020

Klingler Jan-Helge, Elsheikh Samer, Doostkam Soroush, Krüger Marie, Blass Bianca-Ioana, Steiert Christine

PubMed

32389544

Doi

10.1016/j.jocn.2020.05.025

Citation

Klingler J, Elsheikh S, Doostkam S, Krüger M, Blass B, Steiert C. Spinal paraganglioma as unusual finding in von Hippel-Lindau disease. J Clin Neurosci 2020; 77:217-221.

Type

Journal Paper/Review (English)

Journal

J Clin Neurosci 2020; 77

Publication Date

May 7, 2020

Issn Electronic

1532-2653

Pages

217-221

Brief description/objective

A 20-year-old patient with a history of von Hippel-Lindau disease reported on thoracic back pain radiating to the left shoulder for 10 weeks. Magnetic resonance imaging revealed a progressive contrast-enhancing tumor (14 × 21 × 28 mm) compressing the spinal cord and extending into the left neural foramen at T5/6. After embolization of supplying vessels, the tumor was completely resected via hemilaminectomy of T5. The postoperative course was uneventful without surgery related morbidity. The pathological examination disclosed a paraganglioma WHO grade I. We discuss the differential diagnoses and pitfalls of this unexpected finding in this patient with von Hippel-Lindau disease.