Bereiche

Schlagwörter (Tags)

Kontakt

---

Zitation

Art

Name der Konferenz

Veröffentlichungsdatum

Kurzbeschreibung/Zielsetzung

Background and objective: An encephalocele is a congenital disorder of the central nervous system. It occurs with a frequency of 1:3-10.000 births, approximately 90% are located occipital. In occipital encephaloceles about 80% of patients have herniated brain tissue inside the sac which lead to malformation of the remaing brain (stenosis of the aqueductus, hydrocephalus, malformation of venous sinus). The etiology is not yet clear, a neural tube defect is assumed. However most patients have an intact cutaneous coverage which argues against this assumption. Therapy consists of closing the defect, removal of the herniated brain is no longer generally recommended. The prognosis is determined by the degree of brain malformation. The authors present a case with a secondary herniation of brain tissue as seen in MRI