Publikation
Spinal paraganglioma as unusual finding in von Hippel-Lindau disease
Wissenschaftlicher Artikel/Review - 07.05.2020
Klingler Jan-Helge, Elsheikh Samer, Doostkam Soroush, Krüger Marie, Blass Bianca-Ioana, Steiert Christine
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A 20-year-old patient with a history of von Hippel-Lindau disease reported on thoracic back pain radiating to the left shoulder for 10 weeks. Magnetic resonance imaging revealed a progressive contrast-enhancing tumor (14 × 21 × 28 mm) compressing the spinal cord and extending into the left neural foramen at T5/6. After embolization of supplying vessels, the tumor was completely resected via hemilaminectomy of T5. The postoperative course was uneventful without surgery related morbidity. The pathological examination disclosed a paraganglioma WHO grade I. We discuss the differential diagnoses and pitfalls of this unexpected finding in this patient with von Hippel-Lindau disease.