Publikation

European dermatology forum S1-guideline on the diagnosis and treatment of sclerosing diseases of the skin, Part 2: Scleromyxedema, scleredema and nephrogenic systemic fibrosis

Wissenschaftlicher Artikel/Review - 08.08.2017

Bereiche
PubMed
DOI

Zitation
Krieg T, Quaglino P, Petit A, Parodi A, Panelius J, Orteu C, Olszewska M, Krasowska D, Kofoed K, Kárpáti S, Ranki A, Sanchez Schmidt J, Wutte N, Worm M, Wolf P, Tanew A, Taieb A, Sunderkötter C, Sticherling M, Skrok A, Seneschal J, Kähäri V, Just U, Rudnicka L, Denton C, Rongioletti F, Cutolo M, Mouthon L, Cozzio A, Kreuter A, Hunzelmann N, Moinzadeh P, Frasin L, Smith V, Jalili A, Frances C, Foeldvari I, Braae Olesen A, Bouaziz J, Bali G, Bagot M, Aberer E, Gabrielli A, Knobler R. European dermatology forum S1-guideline on the diagnosis and treatment of sclerosing diseases of the skin, Part 2: Scleromyxedema, scleredema and nephrogenic systemic fibrosis. J Eur Acad Dermatol Venereol 2017; 31:1581-1594.
Art
Wissenschaftlicher Artikel/Review (Englisch)
Zeitschrift
J Eur Acad Dermatol Venereol 2017; 31
Veröffentlichungsdatum
08.08.2017
eISSN (Online)
1468-3083
Seiten
1581-1594
Kurzbeschreibung/Zielsetzung

The term 'sclerosing diseases of the skin' comprises specific dermatological entities which have fibrotic changes of the skin in common. These diseases mostly manifest in different clinical subtypes according to cutaneous and extracutaneous involvement and can sometimes be difficult to distinguish from each other. The present guideline focuses on characteristic clinical and histopathological features, diagnostic scores and the serum autoantibodies most useful for differential diagnosis. In addition, current strategies in the first- and advanced-line therapy of sclerosing skin diseases are addressed in detail. Part 2 of this guideline provides clinicians with an overview of the diagnosis and treatment of scleromyxedema, scleredema (of Buschke) and nephrogenic systemic sclerosis (nephrogenic fibrosing dermopathy).