Multifocal adult rhabdomyoma of the head and neck manifestation in 7 locations and review of the literature

Publication

Multifocal adult rhabdomyoma of the head and neck manifestation in 7 locations and review of the literature

Journal Paper/Review - Jun 13, 2013

de Trey Lorraine A, Schmid Stephan, Huber Gerhard

Citation

de Trey L, Schmid S, Huber G. Multifocal adult rhabdomyoma of the head and neck manifestation in 7 locations and review of the literature. Case Rep Otolaryngol 2013; 2013:758416.

Type

Journal Paper/Review (English)

Journal

Case Rep Otolaryngol 2013; 2013

Publication Date

Jun 13, 2013

Issn Print

2090-6765

Pages

758416

Brief description/objective

Background. Adult rhabdomyoma is a rare benign tumour with the differentiation of striated muscle tissue, which mainly occurs in the head and neck region. Twenty-six cases of multifocal adult rhabdomyoma are documented in the literature. Method. We report a 55-year-old male with simultaneous diagnosis of 7 adult rhabdomyomas and review the literature of multifocal adult rhabdomyoma. Result. Review of the literature revealed 26 cases of multifocal adult rhabdomyoma, of which only 7 presented with more than 2 lesions. Mean age at diagnosis was 65 years with a male to female ratio of 5.5 : 1. Common localizations were the parapharyngeal space (36%), larynx (15%), submandibular (14%), paratracheal region (12%), tongue (11%), and floor of mouth (9%). Besides the known radiological features of adult rhabdomyoma, our case showed FDG-uptake in (18) F-FDG PET/CT. Conclusion. This is the first case of multifocal adult rhabdomyoma published, with as many as 7 simultaneous adult rhabdomyomas of the head and neck.